Craniosynostosis

From Paeds.co.uk the online paediatrician's encyclopaedia

Jump to: navigation, search

Craniosynostosis describes premature fusion of one or multiple skull sutures in a child, resulting in abnormal compensatory skull growth and deformity (craniostenosis).

  • Intracranial volume may become limited, resulting in raised intracranial pressure and neurology compromise unless relieved by surgery.


Associated articles:


Contents


Types of Craniosynostosis

See the article Skull Growth Patterns for detailed explanations.

  • Trigonocephaly
  • Brachycephaly
  • Scaphocephaly
  • Plagiocephaly
  • Oxycephaly
  • Kleeblattschaedel


Treatment

Treatment is surgical, usually within the 1st year of life. Each type of craniosynostosis requires a different surgical proceedure and aims to:

  • Prevent secondary cerebral damage
  • Ameliorate other secondary consequences, such as an impaired airway or threatened vision.
  • Improve the cosmetic appearance


The skull shape is correct by mobilising the deformed sutures and fixing them in a better position. Repeat or staged operations may be required.


References

Personal tools
Recommend